History: 9 month old male with urinary tract infection
Solution: Multicystic dysplastic kidney
Uncommon, male predominant (2:1) condition that is more common in infants of diabetic mothers. It is considered sporadic and associated with atresia/obstruction of the ureter prior to 10 weeks of gestational age. Nephrons do not develop normall y and the collecting tubules balloon out into cystic spaces. Can be a palpable abdominal mass, asymptomatic, or associated with symptoms like recurrent urinary tract infections, pain, hematuria, and nausea and vomiting. If bilateral, then it is fatal due to pulmonary hypoplasia. Has a high association with issues in the other kidney like reflux, UPJ obstruction, agenesis, etc.
Imaging findings in this case are classic with numerous cysts of various sizes and shapes with no real residual renal tissue. In this case, the contralateral kidney is normal. The appearance depends on the time and site of the obstruction and the kidney can be small and echogenic with no cysts. Has a rare association with subsequent malignancy. Only remove the kidney if they develop hypertension.
Uncommon, male predominant (2:1) condition that is more common in infants of diabetic mothers. It is considered sporadic and associated with atresia/obstruction of the ureter prior to 10 weeks of gestational age. Nephrons do not develop normall y and the collecting tubules balloon out into cystic spaces. Can be a palpable abdominal mass, asymptomatic, or associated with symptoms like recurrent urinary tract infections, pain, hematuria, and nausea and vomiting. If bilateral, then it is fatal due to pulmonary hypoplasia. Has a high association with issues in the other kidney like reflux, UPJ obstruction, agenesis, etc.
Imaging findings in this case are classic with numerous cysts of various sizes and shapes with no real residual renal tissue. In this case, the contralateral kidney is normal. The appearance depends on the time and site of the obstruction and the kidney can be small and echogenic with no cysts. Has a rare association with subsequent malignancy. Only remove the kidney if they develop hypertension.
Ultrasound Images
